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Case Report

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Platypnea-orthodeoxia-like syndrome in a septic newborn with late appearance of right congenital diaphragmatic hernia

  • GORAZD MLAKAR1
  • STEFAN GROSEK1
  • HELENA MOLE2
  • SILVESTER KOPRIVA1
  • ZIVA ZUPANCIC3
  • JANEZ PRIMOZIC1
  • JANEZ ERZEN4

1,University Medical Centre Ljubljana Department of Paediatric Surgery

2,University Medical Centre Ljubljana Department of Obstetrics and Gynaecology Division of Perinatology

3,University Medical Centre Ljubljana Department of Radiology

4,University Medical Centre Ljubljana Department of Thoracic Surgery

DOI: 10.22514/SV61.042011.10 Vol.6,Issue 1,May 2011 pp.50-52

Published: 02 May 2011

*Corresponding Author(s): STEFAN GROSEK E-mail: stefan.grosek@mf.uni-lj.si

Abstract

Introduction. Cyanosis and dyspnoea with interatrial shunting of blood occurring without change in body position are termed platypnea-orthodeoxia-like syndrome.

Case presentation. We describe a female newborn with sepsis, who developed cyanosis. Two weeks after the initial appe-arance of cyanosis she presented with a right-sided diaphragmatic hernia, which was not seen on the initial X-rays. The hernia was surgically repaired. Her postoperative course was uneventful. 

Conclusions. In our case, interatrial shunting of blood was presumably caused by disturbed intrathoracic pressures. Positive pressure ventilation and sepsis may also contribute to the development of such a syndrome.

Keywords

cyanosis, right-to-left shunt, infant, sepsis, congenital dia-phragmatic hernia 

Cite and Share

GORAZD MLAKAR,STEFAN GROSEK,HELENA MOLE,SILVESTER KOPRIVA,ZIVA ZUPANCIC,JANEZ PRIMOZIC,JANEZ ERZEN. Platypnea-orthodeoxia-like syndrome in a septic newborn with late appearance of right congenital diaphragmatic hernia. Signa Vitae. 2011. 6(1);50-52.

References

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8. Godart F, Rey C, Prat A, Vincentelli A, Chma􀀁¨t A, Francart C, et al. Atrial right-to-left shunting causing severe hypoxemia despite normal right-sided pressures. Eur Heart J 2000;21:483–9.

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